Epitheloid Hemangioendothelioma of the Submandibular Region

Authors

  • Peter Ranjit Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710
  • Parekh Nayan Madhusudan Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710
  • Dayangku Norsuhazenah Pengiran Suhaili Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710
  • Ian Christopher Bickle Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710

DOI:

https://doi.org/10.32412/pjohns.v30i1.391

Keywords:

epitheloid hemangioendothelioma, malignant vascular tumor, submandibular mass

Abstract

Objective: To present an uncommon cause for a submandibular mass and review of the literature.

Methods:

Design: Case Report

Setting: Tertiary Government Hospital

Patient: One

Results: A 25-year-old lady presented with a painless chronic submandibular swelling. Ultrasound identified a solid mass, following which an uncomplicated core biopsy was performed obtaining an accurate pre-operative histopathological diagnosis. Pre-operative arterial embolization of this vascular mass led to a relatively bloodless wide local excision. Radiological imaging for distant metastases was negative.

Conclusion: Epitheloid Hemangioendothelioma is an uncommon cause for a submandibular mass. A malignant vascular soft tissue tumor with morphologic characteristics similar to carcinomas, melanomas and epitheloid sarcomas, it has a high rate of metastasis and morbidity when it affects the soft tissues and viscera. Immunohistochemistry provides clues to differentiation, and recommended treatment consists of a surgical wide local excision with regional lymph node resection. As there are no established standard therapeutic protocols for this disease due to its rarity, an individual case-by-case approach and follow-up needs to be undertaken.

Keywords:  epitheloid hemangioendothelioma, malignant vascular tumor, submandibular mass

Downloads

Download data is not yet available.

Downloads

Published

2015-06-30

How to Cite

1.
Ranjit P, Madhusudan PN, Suhaili DNP, Bickle IC. Epitheloid Hemangioendothelioma of the Submandibular Region. Philipp J Otolaryngol Head Neck Surg [Internet]. 2015 Jun. 30 [cited 2024 Apr. 25];30(1):47-50. Available from: https://pjohns.pso-hns.org/index.php/pjohns/article/view/391

Issue

Vol. 30 No. 1 (2015): Philippine Journal of Otolaryngology-Head and Neck Surgery

Section

Case Reports

License

Copyright transfer (all authors; where the work is not protected by a copyright act e.g. US federal employment at the time of manuscript preparation, and there is no copyright of which ownership can be transferred, a separate statement is hereby submitted by each concerned author). In consideration of the action taken by the Philippine Journal of Otolaryngology Head and Neck Surgery in reviewing and editing this manuscript, I hereby assign, transfer and convey all rights, title and interest in the work, including copyright ownership, to the Philippine Society of Otolaryngology Head and Neck Surgery, Inc. (PSOHNS) in the event that this work is published by the PSOHNS. In making this assignment of ownership, I understand that all accepted manuscripts become the permanent property of the PSOHNS and may not be published elsewhere without written permission from the PSOHNS unless shared under the terms of a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International (CC BY-NC-ND 4.0) license.