Epitheloid Hemangioendothelioma of the Submandibular Region

Authors

  • Peter Ranjit Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710
  • Parekh Nayan Madhusudan Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710
  • Dayangku Norsuhazenah Pengiran Suhaili Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710
  • Ian Christopher Bickle Department of ORL, Level 3, Specialist Building I, RIPAS Hospital Bandar Seri Begawan, Negara Brunei Darussalam, BA1710

DOI:

https://doi.org/10.32412/pjohns.v30i1.391

Keywords:

epitheloid hemangioendothelioma, malignant vascular tumor, submandibular mass

Abstract

Objective: To present an uncommon cause for a submandibular mass and review of the literature.

Methods:

Design: Case Report

Setting: Tertiary Government Hospital

Patient: One

Results: A 25-year-old lady presented with a painless chronic submandibular swelling. Ultrasound identified a solid mass, following which an uncomplicated core biopsy was performed obtaining an accurate pre-operative histopathological diagnosis. Pre-operative arterial embolization of this vascular mass led to a relatively bloodless wide local excision. Radiological imaging for distant metastases was negative.

Conclusion: Epitheloid Hemangioendothelioma is an uncommon cause for a submandibular mass. A malignant vascular soft tissue tumor with morphologic characteristics similar to carcinomas, melanomas and epitheloid sarcomas, it has a high rate of metastasis and morbidity when it affects the soft tissues and viscera. Immunohistochemistry provides clues to differentiation, and recommended treatment consists of a surgical wide local excision with regional lymph node resection. As there are no established standard therapeutic protocols for this disease due to its rarity, an individual case-by-case approach and follow-up needs to be undertaken.

Keywords:  epitheloid hemangioendothelioma, malignant vascular tumor, submandibular mass

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Published

2015-06-30

How to Cite

1.
Ranjit P, Madhusudan PN, Suhaili DNP, Bickle IC. Epitheloid Hemangioendothelioma of the Submandibular Region. Philipp J Otolaryngol Head Neck Surg [Internet]. 2015 Jun. 30 [cited 2024 Nov. 18];30(1):47-50. Available from: https://pjohns.pso-hns.org/index.php/pjohns/article/view/391

Issue

Vol. 30 No. 1 (2015): Philippine Journal of Otolaryngology-Head and Neck Surgery

Section

Case Reports

License

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